Onkologie. 2024:18(2):145-148 | DOI: 10.36290/xon.2024.027
Atypical intradermal smooth muscle tumor (cutaneous leiomyosarcoma): a case report
- Martinské bioptické centrum, s. r. o., Martin
Introduction: Atypical intradermal smooth muscle tumor, also called cutaneous leiomyosarcoma, represents a very rare oncodermatological entity. Due to indolent clinical behaviour it is classified as a tumor of uncertain malignant potential.
Case report: A 63year old man presented with a papular skin tumor arising on the extensor size of the upper part of his left arm. The patient claimed that the lesion had been growing for several years. The tumor was completely removed by surgical excision. Histology revealed an intradermal nodule composed of a solid neoplastic smooth muscle population that exhibits focal nuclear atypia, slightly increased proliferative activity and sporadic mitoses. The diagnosis of atypical intradermal smooth muscle tumor was established. The patient was subsequently referred to oncodispensary care and followed up clinically.
Conclusion: Atypical intradermal smooth muscle tumor/cutaneous leiomyosarcoma is a neoplasm with very favourable prognosis, whose complete surgical removal is curative. An increased risk of local recurrence occurs when the subcutis is involved. However, it is necessary to distinguish it from subcutaneous leiomyosarcoma, which represents an etiologically different and prognostically much more serious oncological disease.
Keywords: atypical intradermal smooth muscle tumor, leiomyosarcoma, pilar leiomyoma.
Accepted: April 19, 2024; Published: May 3, 2024 Show citation
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