Onkologie. 2019:13(4):184-186 | DOI: 10.36290/xon.2019.035
A rare case of adult emybryonal rhabdomyosarcoma
- Oddelenie všeobecnej kardiológie, Stredoslovenský ústav srdcových a cievnych chorôb, a. s. Banská Bystrica
- Kardiochirurgické oddelenie, Stredoslovenský ústav srdcových a cievnych chorôb, a. s. Banská Bystrica
- Patológia, s. r. o. Diagnostické centrum Banská Bystrica
- Pracovisko MRI, Ružomberok
The case report describes a rare case of embryonal rhabdomyosarcoma in adult a 39-year-old male. March 2016 right upper limb amputation in mid-arm for malignant tumor – histology mesenchial tumor with traits v.s. fibrous monophasic synovial sarcoma. Subsequently, two years after the operation, the patient developed heart failure. Echocardiographically a tumor was found around the free wall of the left ventricle (LV) deploying on the LV wall and oppressing the free wall of LV. The finding was also confirmed by the magnetic resonance of the heart. After evaluating the heart team the patient was indicated for cardiac surgery-tumor extirpation. This has been successfully implemented. However, the patient developed severe heart failure in the early post-operative period followed by multiorgan failure and fifth post-operative day patient died. On the basis of complex histomorphological, immunohistochemical and molecular-genetic examination it is embryonal rhabdomyosarcoma (spindle cell subtype high – grade).
Keywords: rhabdomyosarcoma, metastasis, immunohistochemistry, heart failure
Published: September 15, 2019 Show citation
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